Pigmented Dermatofibrosarcoma Protuberans (Bednar Tumor) masquerading clinically as malignant melanoma - A Case Report
Keywords:
Dermatofibrosarcoma protuberance (DFSP), Bednar tumour, Malignant Melanoma
Abstract
Bednar tumor is a rare neoplasm of intermediate malignant potential, which account for less than 5% of dermatofibrosarcoma protuberans (DFSP).This tumor is a pigmented variant of DFSP. The diagnosis is commonly made in early to mid adult life except in cases with melanin containing cells. The case report presents a 19 years old female who presented with a painless slow-growing 3.5×3×1.2 cm blackish mass on the dorsal aspect of her right foot. Histopathological examination of the biopsy specimen revealed typical features of a Bednar tumor, the diagnosis was confirmed through immunohistochemical study. DOI: 10.21276/AABS.2017.1279References
1. Kaburagi Y, Hatta N, Kawara S, Takehara K. Pigmented dermatofibrosarcoma
protuberans (Bednar tumor) occurring in a Japanese infant. Dermatology 1998; 197: 48-51.
2. Dupree WB, Langloss JM, Weiss SW. Pigmented dermatofibrosarcoma protuberans (Bednar tumor). A pathologic, ultrastructural, and immunohistochemical study. Am J Surg Pathol 1985; 9: 630-9.
3. Fletcher C D M, Theaker J M, Flanagan A et al. Pigmented dermatofibrosarcoma protuberans (Bednar tumour): melanocytic colonization or neuroectodermal differentiation? A clinicopathological and immunohistochemical study. Histopathology1988;13:631-43
4. Aiba S, Tabata N, Ishi H et al. Dermatofibrosarcoma protuberans
is a unique fibrohistiocytic tumor expressing CD34.Br J Dermatol 1992;127: 79-84
5. Brathwaite C, Suster S Dermatofibrosarcoma protuberans:a critical reappraisal of the role of immunohistochemical stains for diagnosis. Appl Immunohistochem 1994;2: 36-41
6. Kagoura M, Toyoda M, Nagahori H, Makino T, Morohashi M. An ultrastructural and immunohistochemical study of pigmented dermatofibrosarcoma protuberans (Bednar tumor). Eur J Dermatol. 1999; 9: 366-9.
7. Vandeweyer E, Deraemaecker R, Somerhausen ND,Geledan L, Gebhart M. Bednar tumor of the foot: a case report. Foot Ankle Int. 2001; 22:339-41.
8. Reis-Filho JS, Milanezi F, Ferro J, Schmitt FC. Pediatric pigmented
dermatofibrosarcoma protuberans (Bednar tumor): case report and
review of the literature with emphasis on the differential diagnosis. Pathol Res Pract 2002; 198: 621-6.
9. Marcus JR, Few JW, Senger C, Reynolds M. Dermatofibrosarcoma
protuberans and the Bednar tumor: treatment in the pediatric population.
J Pediatr Surg 1998; 33: 1811-4.
10. Mochizuki Y, Narisawa Y, Kohda H. A case of Bednar tumor recurring
after 23 years. J Dermatol 1996; 23: 614-8.
protuberans (Bednar tumor) occurring in a Japanese infant. Dermatology 1998; 197: 48-51.
2. Dupree WB, Langloss JM, Weiss SW. Pigmented dermatofibrosarcoma protuberans (Bednar tumor). A pathologic, ultrastructural, and immunohistochemical study. Am J Surg Pathol 1985; 9: 630-9.
3. Fletcher C D M, Theaker J M, Flanagan A et al. Pigmented dermatofibrosarcoma protuberans (Bednar tumour): melanocytic colonization or neuroectodermal differentiation? A clinicopathological and immunohistochemical study. Histopathology1988;13:631-43
4. Aiba S, Tabata N, Ishi H et al. Dermatofibrosarcoma protuberans
is a unique fibrohistiocytic tumor expressing CD34.Br J Dermatol 1992;127: 79-84
5. Brathwaite C, Suster S Dermatofibrosarcoma protuberans:a critical reappraisal of the role of immunohistochemical stains for diagnosis. Appl Immunohistochem 1994;2: 36-41
6. Kagoura M, Toyoda M, Nagahori H, Makino T, Morohashi M. An ultrastructural and immunohistochemical study of pigmented dermatofibrosarcoma protuberans (Bednar tumor). Eur J Dermatol. 1999; 9: 366-9.
7. Vandeweyer E, Deraemaecker R, Somerhausen ND,Geledan L, Gebhart M. Bednar tumor of the foot: a case report. Foot Ankle Int. 2001; 22:339-41.
8. Reis-Filho JS, Milanezi F, Ferro J, Schmitt FC. Pediatric pigmented
dermatofibrosarcoma protuberans (Bednar tumor): case report and
review of the literature with emphasis on the differential diagnosis. Pathol Res Pract 2002; 198: 621-6.
9. Marcus JR, Few JW, Senger C, Reynolds M. Dermatofibrosarcoma
protuberans and the Bednar tumor: treatment in the pediatric population.
J Pediatr Surg 1998; 33: 1811-4.
10. Mochizuki Y, Narisawa Y, Kohda H. A case of Bednar tumor recurring
after 23 years. J Dermatol 1996; 23: 614-8.
Published
2017-02-03
Issue
Section
Case Reports
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