Hereditary Ectodermal Dysplasia: A Case Report

  • Virender Kumar DR HSJ INSTITUTE OF DENTAL SCIENCE AND HOSPITAL
  • Lalit Kumar DR HSJ INSTITUTE OF DENTAL SCIENCE AND HOSPITAL
Keywords: Ectodermal Dysplasia (ED), Hypohidrotic, Hypodontia

Abstract

Ectodermal dysplasia (ED) is a hereditary disease characterized by anomalies in the structures of ectodermal origin. The disease affects skin, saliva, sebaceous and sweat glands (anhidrosis or hypohidrosis), hair (atrichosis or hypotrichosis), nail and teeth (anodontia or hypodontia). Oral rehabilitation is important from a functional, esthetic and psychological standpoint. A team approach, that includes input from Peadodontist, an Orthodontist, a Prosthodontist and an Oral and maxillofacial surgeon, is necessary for a successful outcome. This paper discusses a case of Hypohidrotic Ectodermal Dysplasia and its management.

Author Biographies

Virender Kumar, DR HSJ INSTITUTE OF DENTAL SCIENCE AND HOSPITAL
ASSISTANT PROFESSORDEPARTMENT OF PROSTHODONTICS
Lalit Kumar, DR HSJ INSTITUTE OF DENTAL SCIENCE AND HOSPITAL
ASSOCIATE PROFESSORDEPARTMENT OF PROSTHODONTICS

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Published
2015-09-02
Section
Case Reports