Peutz-Jegher's syndrome: A diagnosis clinched on histopathology

  • Somshamkar Chowdhury
  • Neha Tyagi Senior resident Department of pathology,VMMC and Safdarjung Hospital.New Delhi
  • Leelawathi Dawson
  • Ashish K Mandal
Keywords: Peutz-Jegher's syndrome, Autosomal, Malignancy,


Peutz Jeghers syndrome (PJS) is an inherited autosomal dominant disorder characterised by hamartomatous polyp in the gastrointestinal tract and pigmented mucocutaneous lesion. Data on prevalence of PJS in India is not available. PJS predisposes sufferers to various malignancies (gastrointestinal, pancreatic, lung, breast, uterine, ovarian and testicular tumours).we report here a case  of 18 year old male with Peutz Jeghers syndrome.


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