A Case of Clear Cell Sarcoma of Kidney in An Adult: An Extremely Rare Presentation

  • Pragya Nirav Vakani Nirmaan Pathology Laboratory, Ahmedabad, Gujarat, India
  • Mukesh Maheshwari Nirmaan Pathology Laboratory, Ahmedabad, Gujarat, India
  • Jainil Maheshwari NHL Medical College, Ahmedabad, Gujarat, India
  • Anshul Agarwal Nirmaan Pathology Laboratory, Ahmedabad, Gujarat, India
  • Pragnesh Patel Deep Urosurgical Hospital, Ahmedabad, Gujarat, India
  • Chandresh Shah Deep Urosurgical Hospital, Ahmedabad, Gujarat, India
Keywords: Clear cell sarcoma of the kidney (CCSK), Immunohistochemistry (IHC), Kidney.

Abstract

Clear cell sarcoma of the kidney (CCSK) is a malignant renal tumor of childhood with a propensity to metastasize to bone and other organs. It is extremely rare in adults, must be differentiated from clear cell carcinoma of kidney which is more common in adults. We report a case of CCSK in a 45 year old female, confirmed by Immunohistochemistry (IHC) & managed with radical nephrectomy. The aim of this case report is to increase the awareness about this entity in adults with brief review of relevant literature.

Author Biographies

Pragya Nirav Vakani, Nirmaan Pathology Laboratory, Ahmedabad, Gujarat, India
Department of Pathology
Mukesh Maheshwari, Nirmaan Pathology Laboratory, Ahmedabad, Gujarat, India
Department of Pathology
Jainil Maheshwari, NHL Medical College, Ahmedabad, Gujarat, India
Research Student
Anshul Agarwal, Nirmaan Pathology Laboratory, Ahmedabad, Gujarat, India
Department of Pathology
Pragnesh Patel, Deep Urosurgical Hospital, Ahmedabad, Gujarat, India
Department of Urology
Chandresh Shah, Deep Urosurgical Hospital, Ahmedabad, Gujarat, India
Department of Urology

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Published
2018-09-17
Section
Case Report