Persistent Mullerian Duct Syndrome

A Case Report

  • Shabnam Izhar Vivekananda Polyclinic Institute of Medical Science(VPIMS), Lucknow, India
  • Purnima Singh Vivekananda Polyclinic Institute of Medical Science(VPIMS), Lucknow, India
  • Kusum Gupta Vivekananda Polyclinic Institute of Medical Science(VPIMS), Lucknow, India
DOI: https://doi.org/10.21276/apalm.2559
Keywords: Mullerian inhibiting substances, hernia uteri inguinale, persistent Mullerian duct syndrome.

Abstract

Persistent Mullerian duct syndrome (PMDS) is usually an accidental finding either during orchidopexy or during routine inguinal hernia repair in male patients presenting with undescended testes. It is a rare form of internal male pseudohermaphroditism caused by defect in synthesis or action of Mullerian inhibiting factor due to which Mullerian derivatives such as uterus, fallopian tube and upper vagina are normally present in 46XY males. Here we present a case report of a 7 year old male presenting with bilateral undescended testes.

Author Biographies

Shabnam Izhar, Vivekananda Polyclinic Institute of Medical Science(VPIMS), Lucknow, India
Department of Pathology
Purnima Singh, Vivekananda Polyclinic Institute of Medical Science(VPIMS), Lucknow, India
Department of Pathology
Kusum Gupta, Vivekananda Polyclinic Institute of Medical Science(VPIMS), Lucknow, India
Department of Pathology

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Published
2019-08-26
Issue
Vol 6 No 8 (2019)
Section
Case Report

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