Rare Neurogenic Tumor - Pacinian Neurofibroma

A Case Report

Authors

  • Shivani Panhotra Hamdard Institute of Medical Sciences and Research, Jamia Hamdard, New Delhi 110062, India
  • Zeeba S Jairajpuri Hamdard Institute of Medical Sciences and Research, Jamia Hamdard, New Delhi 110062, India
  • Beenish Sultan Hamdard Institute of Medical Sciences and Research, Jamia Hamdard, New Delhi 110062, India
  • Sujata Jetley Hamdard Institute of Medical Sciences and Research, Jamia Hamdard, New Delhi 110062, India
  • Nehal Ahmad Hamdard Institute of Medical Sciences and Research, Jamia Hamdard, New Delhi 110062, India

DOI:

https://doi.org/10.21276/apalm.2693

Keywords:

Pacinian neurofibroma, Pacinian corpuscles, S-100 antibodies

Abstract

Pacinian neurofibroma (PN), a rare benign dermal tumor characterized by proliferation of pacinian corpuscles in the dermal myxoid stroma. A 50 year female presented with slow growing, soft, painless swelling over right wrist. No other significant history was found. Histopathology revealed proliferation of fibrous connective tissue along with whorled structures. No cellular atypia was found. Immunohistochemistry examination with antibodies against protein S-100 showed diffuse positivity. A diagnosis of Pacinian neurofibroma was made.

Author Biographies

  • Shivani Panhotra, Hamdard Institute of Medical Sciences and Research, Jamia Hamdard, New Delhi 110062, India

    Department of Pathology

  • Zeeba S Jairajpuri, Hamdard Institute of Medical Sciences and Research, Jamia Hamdard, New Delhi 110062, India

    Department of Pathology

  • Beenish Sultan, Hamdard Institute of Medical Sciences and Research, Jamia Hamdard, New Delhi 110062, India

    Department of Pathology

  • Sujata Jetley, Hamdard Institute of Medical Sciences and Research, Jamia Hamdard, New Delhi 110062, India

    Department of Pathology

  • Nehal Ahmad, Hamdard Institute of Medical Sciences and Research, Jamia Hamdard, New Delhi 110062, India

    Department of Pathology

References

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Published

12-03-2020

Issue

Section

Case Report

How to Cite

1.
Rare Neurogenic Tumor - Pacinian Neurofibroma: A Case Report. Ann of Pathol and Lab Med [Internet]. 2020 Mar. 12 [cited 2025 Dec. 13];7(2):C35-37. Available from: https://pacificejournals.com/journal/index.php/apalm/article/view/2693