Paratesticular Embryonal Rhabdomyosarcoma with Lung Metastasis – A Rare Case Report

  • Anusha Ganapathi Department of Pathology, Sri Ramachandra Institute of Higher Education and Research, Chennai, Tamil Nadu, India
  • Thanka J Department of Pathology, Sri Ramachandra Institute of Higher Education and Research, Chennai, Tamil Nadu, India
  • Lawrence D'Cruze Department of Pathology, Sri Ramachandra Institute of Higher Education and Research, Chennai, Tamil Nadu, India
  • Barathi G Department of Pathology, Sri Ramachandra Institute of Higher Education and Research, Chennai, Tamil Nadu, India
  • Natarajan K Department of Pathology, Sri Ramachandra Institute of Higher Education and Research, Chennai, Tamil Nadu, India
  • Julius Xavier Scott Department of Paediatric Hemato-oncology, Sri Ramachandra Institute of Higher Education and Research, Chennai, Tamil Nadu, India.
Keywords: Paratesticular RMS, Embryonal, Lung Metastasis, Myogenin

Abstract

Paratesticular rhabdomyosarcomas (RMS) are very rare malignant tumors arising from the mesenchymal tissues of tunica, epididymis or spermatic cord. They present as painless hard masses in inguinoscrotal region, and large tumors can be mistaken for testicular tumors. They can spread to retroperitoneal lymph nodes or hematogenously metastasize to lung, bones and bone marrow. Here, we report a case of Embryonal RMS with spindle cell component presenting with painless scrotal mass and lung metastasis at initial diagnosis.

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Published
2020-11-30
Section
Case Report