Angiomyxoma of the Lower Eyelid with Orbital Extension: A Rare Entity and Review of Literature

  • Sahil Agrawal Dr. Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences New Delhi –110 029, India
  • Aarush Deora Dr. Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences New Delhi –110 029, India
  • Sujeeth Modaboyina Dr. Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences New Delhi –110 029, India
  • Deepsekhar Das Dr. Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences New Delhi –110 029, India
  • Mandeep Singh Bajaj Dr. Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences New Delhi –110 029, India
  • Seema Sen Department of Ocular Pathology, All India Institute of Medical Sciences, New Delhi –110 029, India
Keywords: Angiomyxoma, orbital tumor, proptosis, lid tumor, Carneys complex

Abstract

A 60-year-old male sought medical advice for painless progressive swelling in the left eye associated with protrusion of the eyeball and diminution of vision for the past 6 months. A computed tomography scan was done which revealed a heterogeneous lesion in the inferotemporal orbit lying close to the globe without any bony erosions or intracranial extension. Incisional biopsy revealed spindle or stellate cells in a myxoid matrix with abundant thin-walled vessels. On Immunohistochemistry, the tumour was positive for vimentin and SMA. It was negative for Desmin and S-100. A diagnosis of superficial angiomyxoma of the eyelid with orbital extension was thus made. Surgical excision under general anaesthesia was planned and the mass removed in toto. The histopathological examination of the same revealed findings similar to the incision biopsy. The patient is being followed up with no recurrences till date.

References

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Published
2021-05-10
Section
Case Report