Melorheostosis: A Case Report in Pediatric Age Group

  • Rakesh Mehra Department of Pathology, Patna Medical College Hospital (PMCH), Ashok Rajpath, Patna, Bihar, India
  • Richa Bhartiya Department of Pathology, Patna Medical College Hospital (PMCH), Ashok Rajpath, Patna, Bihar, India
  • Pallavi Agrawal Dept. of Pathology, Patna Medical College & Hospital (PMCH), Ashok Rajpath, Patna Bihar India PIN-800004
Keywords: Sclerotic Bone Dysplasia, Cytology, Biopsy, FNAC

Abstract

Melorheostosis is a rare, benign, and disabling condition. It is a rare mesenchymal bone disease classified as a sclerotic bone dysplasia. We present this case because of its rarity and highlight the importance of Fine needle aspiration cytology which is a minimally invasive technique in ruling out the possibilities of osteomyelitis and malignancies. Fine Needle Aspiration Cytology (FNAC) negates the use of unwarranted biopsies. The disease is a benignentity with a generally chronic course and periods of exacerbation and remission. Therapy is symptomatic and is aimed at controlling pain.  DOI: 10.21276/APALM.1205

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Published
2017-10-19
Section
Case Report