Primary Systemic Amyloidosis: A Case Report

  • Tanima Dwivedi Post Graduate, Department of Pathology, KLE University’s J.N. Medical College, Belgaum, Karnataka(India)-590010
  • Ramesh Chavan Professor, Department of Pathology, KLE University’s J.N.Medical college, Belgaum, Karnataka(India)-590010
Keywords: primary systemic amyloidosis, Idiopathic, plasma cell dyscrasia, AL amyloidosis

Abstract

Primary systemic amyloidosis is a rare entity. We report a case of primary systemic primary amyloidosis, an elderly male presented with generalized weakness since 6 months. Clinical examination revealed typical waxy lesions in the periorbital area with macroglossia. Serum electrophoresis was normal, however, bone marrow examination showed increased plasma cell with a good number of both binucleated and immature plasma cells. Diagnosis was confirmed by skin biopsy using haemotoxylin & eosin staining and congo red staining. Polarised microscopy was not done because of unavailability. We present the myriad manifestations of this uncommon disease entity.

Author Biographies

Tanima Dwivedi, Post Graduate, Department of Pathology, KLE University’s J.N. Medical College, Belgaum, Karnataka(India)-590010
post graduate, pathology
Ramesh Chavan, Professor, Department of Pathology, KLE University’s J.N.Medical college, Belgaum, Karnataka(India)-590010
Professor, Department of Pathology, KLE University’s J.N.Medical College,Belagavi,Karnataka(India)-590010 

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Published
2016-02-25
Issue
Vol 3 No 1 (2016)
Section
Case Report

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