Steroid Cell Tumor of Ovary Not Otherwise Specified in A Child
Keywords:
Ovarian tumors, Androgenic manifestations
Abstract
Steroid cell tumour of the ovary is a very rare sex cord stromal tumour of ovary which commonly presents in women belonging to third and fourth decade of life. It usually manifests with a pelvic mass along with androgenic symptoms. We present a case of 3 year old child, who presented with precocious puberty and hirsutism. Radiology was suggestive of ovarian mass for which oophorectomy was done. Gross, histopathological examination and immunohistochemistry proved it to be a steroid cell tumour, not otherwise specified. Our case being unique because of presentation at merely 3 years of age.References
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[3] Dinc G, Saygin I, Kart C, Mungan S, Guven S, Seda Guvendag Guven E. A rare case of postmenopausal severe virilization: Ovarian steroid cell tumour, not otherwise specified. J Cases Obstet Gynecol. 2016;3(1):19-21.
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[5]Hayes MC, Scully RE. Ovarian steroid cell tumours (not otherwise specified): A clinic-pathological analysis of 63 cases. Am J Surg Pathol. 1987;11(11):835–45.
[6] Mehdi G, Ansari HA, Sherwani RK, Rahman K, Akhtar N. Ovarian Steroid Cell Tumour: Correlation of Histopathology with Clinico-pathologic Features. Pathology Research International. Volume 2011, Article ID 987895, 5 pages.
[7] Rabban JT, Zaloudek CJ. A practical approach to immunohistochemical diagnosis of ovarian germ cell tumours and sex cord-stromal tumours. Histopathology. 2013 Jan;62(1):71–88.
[8] Jiang W, Tao X, Fang F, Zhang S, Xu C. Benign and malignant ovarian steroid cell tumours, not otherwise specified: case studies, comparison, and review of the literature. Journal Of Ovarian Research. 2013,6:53.
[9] Swain J, Sharma S, Prakash V, Agrawal NK, Singh SK. Steroid cell tumour: a rare cause of hirsutism in a female. Endocrinology, Diabetes and Metabolism case reports. September 2013;ID 13-0030.
[10] R.E. Scully . Ovarian tumours. A review. Am J Pathol. 1977 Jun;87(3):686-720.
[11] Lee SH, Kang MS, Lee GS, Chung WY. Refractory Hypertension and Isosexual Pseudoprecocious Puberty Associated with Renin-Secreting Ovarian Steroid Cell Tumor in a Girl. J Korean Med Sci. 2011 Jun;26(6):836-838.
[2] Qian L, Shen Z, Zhang X, Wu D, & Zhou Y. Ovarian steroid cell tumor, not otherwise specified: A case report and literature review. Molecular and clinical oncology.2016 Dec, 5(6):839–841.
[3] Dinc G, Saygin I, Kart C, Mungan S, Guven S, Seda Guvendag Guven E. A rare case of postmenopausal severe virilization: Ovarian steroid cell tumour, not otherwise specified. J Cases Obstet Gynecol. 2016;3(1):19-21.
[4] Outwater EK, Wagner BJ, Mannion C, McLarney JK, Kim B. Sex cord-stromal and steroid cell tumours of the ovary. .Radiographics. 1998 Nov- Dec; 18(6):1523-46.
[5]Hayes MC, Scully RE. Ovarian steroid cell tumours (not otherwise specified): A clinic-pathological analysis of 63 cases. Am J Surg Pathol. 1987;11(11):835–45.
[6] Mehdi G, Ansari HA, Sherwani RK, Rahman K, Akhtar N. Ovarian Steroid Cell Tumour: Correlation of Histopathology with Clinico-pathologic Features. Pathology Research International. Volume 2011, Article ID 987895, 5 pages.
[7] Rabban JT, Zaloudek CJ. A practical approach to immunohistochemical diagnosis of ovarian germ cell tumours and sex cord-stromal tumours. Histopathology. 2013 Jan;62(1):71–88.
[8] Jiang W, Tao X, Fang F, Zhang S, Xu C. Benign and malignant ovarian steroid cell tumours, not otherwise specified: case studies, comparison, and review of the literature. Journal Of Ovarian Research. 2013,6:53.
[9] Swain J, Sharma S, Prakash V, Agrawal NK, Singh SK. Steroid cell tumour: a rare cause of hirsutism in a female. Endocrinology, Diabetes and Metabolism case reports. September 2013;ID 13-0030.
[10] R.E. Scully . Ovarian tumours. A review. Am J Pathol. 1977 Jun;87(3):686-720.
[11] Lee SH, Kang MS, Lee GS, Chung WY. Refractory Hypertension and Isosexual Pseudoprecocious Puberty Associated with Renin-Secreting Ovarian Steroid Cell Tumor in a Girl. J Korean Med Sci. 2011 Jun;26(6):836-838.
Published
2020-05-28
Issue
Section
Case Report
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