Intratesticular Rhabdomyosarcoma- A Rare Childhood Tumour
Abstract
Primary malignant of tumours of the testis are rare in children. Tumours of germ cell origin account for 60-77% of primary testicular tumors. Intrascrotal tumours of nongerm cell origin are rare. Rhabdomyosarcomas (RMS) are the commonest tumours among nongerm cell tumours. RMS are more commonly seen in paratesticular region. Pure testicular RMS are rare. A 16 yr boy was evaluated right sided testicular mass. Histopathology and immunohistochemistry confirmed it to be an anaplastic embryonal rhabdomyosarcoma. Here we report this case with a brief review of literature.References
Dagher R and Helman L: Rhabdomyosarcoma: An overview. Oncologist 4: 34 44, 1999
Siwillis EM, Dharse NJ, Scanlan T, Ngoma M, Abraham ZS, Kahiu JW, et al.Pediatric soft tissue and bone sarcomas in Tanzania: epidemiology and clinical features. J Glob Oncol. 2019;5:1–6.
Venyo AK-G. Rhabdomyosarcoma of the testis, epididymis and spermatic cord: A review and update. Pulsus J Surg Res. 2018;2:435–41.
Ciftci A O, Bingo M, lu I K, Mehmet E. S¸ Enocak, F. Tanyel C et al. Testicular tumours in children. J paediatr Surg.2001:36;1796-81
Rudzinski E R, Anderson J R, Hawkins D S, Skapek S X, Parham D M, Teot MA. The World Health Organization Classification of Skeletal Muscle Tumors in Pediatric Rhabdomyosarcoma: A Report From the Children’s Oncology Group. Arch Pathol Lab Med. 2015 October ; 139: 1281–1287.
Kelly B, Lundon D, Rowaiye B, Daly P, Walsh K. Embryonal rhabdomyosarcoma of the testis. Canad Urol Assoc J. 2011;5:E7.
Manasseh AN, Echejoh GO, Silas OA, Tanko MN, Jegede SK, Mandong BM. Testicular embryonal rhabdomyosarcoma: A case Report. Int J Med Med Sci 2009;1:470-2.
Nasit JG, Parikh B, Trivedi P, Shah M. Primary intratesticular rhabdomyosarcoma in pediatrics. Ind J Urol. 2013;29:77.
Yi J, Zhou D A, Huo JR, Wang Y N , Ma J N. Primary intratesticular rhabdomyosarcoma: A case report and literature review. Oncol lettrs.2016;11:1016-20
Anusha G, Thanka J, D’CruzeL, Barathi G, Natarajan K, Scott JX. Paratesticular Embryonal Rhabdomyosarcoma with Lung Metastasis – A Rare Case Report. APALM 2020;7:164-7.
Parham DM, Ellison DA. Rhabdomyosarcomas in adults and children: an update. Arch Pathol Lab Med. 2006;130:1454-65
Hamilton CR, Pinkerton R, and Horwich A: The management of paratesticular rhabdomyosarcoma. Clin Radiol .1989;40: 314 –317,
Ruymann FB, Grovas AC. Progress in the diagnosis and treatment of rhabdomyosarcoma and related soft tissue sarcomas. Cancer Invest.2000;18:223–41.
Copyright (c) 2022 Hilda Fernandes, Netheya Mary Thomas, Anush Serrao
This work is licensed under a Creative Commons Attribution 4.0 International License.
Authors who publish with this journal agree to the following terms:
- Authors retain copyright and grant the journal right of first publication with the work simultaneously licensed under a Creative Commons Attribution License that allows others to share the work with an acknowledgement of the work's authorship and initial publication in this journal.
- Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal.
- Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work (See The Effect of Open Access at http://opcit.eprints.org/oacitation-biblio.html).
